Family conditions and dietary control in phenylketonuria

• Objective This investigation is an attempt to describe coping with phenylketonuria (PKU) in order to understand some aspects underlying good compliance. Methods The coping concept was applied to PKU in two questionnaires. Self- and parental ratings were combined with assessments of phenylalanine levels and the severity of the disease. All Swedish patients with PKU born in 1980–91, a total of 53 children and youths with their parents, were invited to participate in the study and 41 (77%) of them did so. Results The patients turned out to have good compliance with the diet. The main result was that patients with separated or divorced parents were more likely to have higher phenylalanine levels and this association was not diminished by adjustment for the potential confounding factors. Conclusion Patients’ need for support must be judged individually according to different family conditions.

Ämnesord

MEDICIN OCH HÄLSOVETENSKAP  -- Klinisk medicin (hsv//swe)

MEDICAL AND HEALTH SCIENCES  -- Clinical Medicine (hsv//eng)

MEDICIN OCH HÄLSOVETENSKAP  -- Medicinska och farmaceutiska grundvetenskaper -- Cell- och molekylärbiologi (hsv//swe)

MEDICAL AND HEALTH SCIENCES  -- Basic Medicine -- Cell and Molecular Biology (hsv//eng)

Nyckelord

Adaptation; Psychological

Adolescent

Adolescent Psychology

Attitude to Health

Child

Child Psychology

Chronic Disease

Divorce/psychology

Family Characteristics

Female

Humans

Logistic Models

Male

Odds Ratio

Patient Compliance/*psychology

Phenylalanine/blood

Phenylketonurias/blood/*diet therapy/*psychology

Questionnaires

Severity of Illness Index

Stress; Psychological

Sweden

Molecular medicine

genetics

pathology

MEDICINE

MEDICIN

Internal medicine

Invärtesmedicin

Invärtesmedicin

Internal Medicine

Publikations- och innehållstyp

ref (ämneskategori)

art (ämneskategori)