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Risk stratification in chronic thromboembolic pulmonary hypertension predicts survival

Sandqvist, Anna (författare)
Umeå University,Umeå universitet,Institutionen för farmakologi och klinisk neurovetenskap,Actelion a Division of Janssen-Cilag AB, Stockholm, Sweden,Department of Pharmacology and Clinical Neuroscience, Umeå University, Umeå, Sweden; Janssen-Cilag AB, Stockholm, Sweden,Umeå Univ, Dept Pharmacol & Clin Neurosci, Umeå, Sweden.;Janssen Cilag AB, Actelion Div, Stockholm, Sweden.
Kylhammar, David (författare)
Linköpings universitet,Linköping University,Avdelningen för diagnostik och specialistmedicin,Medicinska fakulteten,Region Östergötland, Fysiologiska kliniken US,Linköping Univ, Dept Med & Hlth Sci, Linköping, Sweden.;Linköping Univ, Dept Clin Physiol, Linköping, Sweden.
Bartfay, Sven-Erik (författare)
Gothenburg University,Göteborgs universitet,University of Gothenburg,Department of Medicine, Sahlgrenska Academy, Gothenburg University, Gothenburg, Sweden; Department of Cardiology, Sahlgrenska University Hospital, Gothenburg, Sweden,Gothenburg Univ, Sahlgrenska Acad, Dept Med, Gothenburg, Sweden.;Sahlgrens Univ Hosp, Dept Cardiol, Gothenburg, Sweden.,Institutionen för medicin, avdelningen för molekylär och klinisk medicin,Institute of Medicine, Department of Molecular and Clinical Medicine
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Hesselstrand, Roger (författare)
Lund University,Lunds universitet,Forskargruppen för systemisk skleros, Lund,Forskargrupper vid Lunds universitet,Lund Systemic Sclerosis Research Group,Lund University Research Groups,Department of Clinical Sciences Section of Rheumatology, Lund University, Lund, Sweden,Lund Univ, Dept Clin Sci, Sect Rheumatol, Lund, Sweden.
Hjalmarsson, Clara, 1969 (författare)
Gothenburg University,Göteborgs universitet,University of Gothenburg,Department of Medicine, Sahlgrenska Academy, Gothenburg University, Gothenburg, Sweden; Department of Cardiology, Sahlgrenska University Hospital, Gothenburg, Sweden,Gothenburg Univ, Sahlgrenska Acad, Dept Med, Gothenburg, Sweden.;Sahlgrens Univ Hosp, Dept Cardiol, Gothenburg, Sweden.,Institutionen för medicin, avdelningen för molekylär och klinisk medicin,Institute of Medicine, Department of Molecular and Clinical Medicine
Kavianipour, Mohammad (författare)
Umeå University,Umeå universitet,Kardiologi,Department of Public Health and Clinical Medicine, Sundsvall Research Unit, Umeå University, Umeå, Sweden,Umeå Univ, Dept Publ Hlth & Clin Med, Sundsvall Res Unit, Umeå, Sweden.
Nisell, Magnus (författare)
Department of Medicine Solna, Karolinska Institute, Karolinska University Hospital, Stockholm, Sweden; The Department of Respiratory Medicine and Allergy, Karolinska University Hospital, Stockholm, Sweden,Karolinska Univ Hosp, Karolinska Inst, Dept Med Solna, Stockholm, Sweden.;Karolinska Univ Hosp, Dept Resp Med & Allergy, Stockholm, Sweden.
Rådegran, Göran (författare)
Lund University,Lunds universitet,Lund Hemodynamic Lab,Forskargrupper vid Lunds universitet,Lund University Research Groups,Department of Clinical Sciences Lund, Cardiology, Lund University, Lund, Sweden; The Section for Heart Failure and Valvular Disease, VO Heart and Lung Medicine, Skåne University Hospital, Lund, Sweden,Lund Univ, Dept Clin Sci Lund, Cardiol, Lund, Sweden.;Skane Univ Hosp, Sect Heart Failure & Valvular Dis, VO Heart & Lung Med, Lund, Sweden.
Wikström, Gerhard (författare)
Uppsala universitet,Uppsala University,Department of Medical Sciences, Cardiology, Uppsala University, Uppsala University Hospital, Uppsala, Sweden,Kardiologi,Uppsala kliniska forskningscentrum (UCR)
Kjellström, Barbro (författare)
Karolinska Institutet,Karolinska Institute,Lund University,Lunds universitet,Klinisk fysiologi, Lund,Sektion V,Institutionen för kliniska vetenskaper, Lund,Medicinska fakulteten,Clinical Physiology (Lund),Section V,Department of Clinical Sciences, Lund,Faculty of Medicine,Department of Medicine, Cardiology Unit, Karolinska Institute, Stockholm, Sweden; Department of Clinical Sciences Lund, Clinical Physiology, Lund University, Lund, Sweden; Skåne University Hospital, Lund, Sweden,Karolinska Inst, Dept Med, Cardiol Unit, Stockholm, Sweden.;Lund Univ, Dept Clin Sci Lund, Clin Physiol, Lund, Sweden.;Skane Univ Hosp, Lund, Sweden.
Söderberg, Stefan (författare)
Umeå University,Umeå universitet,Avdelningen för medicin,Department of Public Health and Clinical Medicine, and Heart Centre, Umeå University, Umeå, Sweden,Umeå Univ, Dept Publ Hlth & Clin Med, SE-90187 Umeå, Sweden.;Umeå Univ, Heart Ctr, Umeå, Sweden.
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 (creator_code:org_t)
2020-06-26
2021
Engelska.
Ingår i: Scandinavian Cardiovascular Journal. - : Taylor & Francis Group. - 1401-7431 .- 1651-2006. ; 55:1, s. 43-49
  • Tidskriftsartikel (refereegranskat)
Abstract Ämnesord
Stäng  
  • Objectives: To investigate if the pulmonary arterial hypertension (PAH) risk assessment tool presented in the 2015 ESC/ERS guidelines is valid for patients with chronic thromboembolic pulmonary hypertension (CTEPH) when taking pulmonary endarterectomy (PEA) into account. Design. Incident CTEPH patients registered in the Swedish PAH Registry (SPAHR) between 2008 and 2016 were included. Risk stratification performed at baseline and follow-up classified the patients as low-, intermediate-, or high-risk using the proposed ESC/ERS risk algorithm. Results: There were 250 CTEPH patients with median age (interquartile range) 70 (14) years, and 53% were male. Thirty-two percent underwent PEA within 5 (6) months. In a multivariable model adjusting for age, sex, and pharmacological treatment, patients with intermediate-risk or high-risk profiles at baseline displayed an increased mortality risk (Hazard Ratio [95% confidence interval]: 1.64 [0.69–3.90] and 5.39 [2.13–13.59], respectively) compared to those with a low-risk profile, whereas PEA was associated with better survival (0.38 [0.18–0.82]). Similar impact of risk profile and PEA was seen at follow-up.Conclusion: The ESC/ERS risk assessment tool identifies CTEPH patients with reduced survival. Furthermore, PEA improves survival markedly independently of risk group and age.

Ämnesord

MEDICIN OCH HÄLSOVETENSKAP  -- Klinisk medicin -- Kardiologi (hsv//swe)
MEDICAL AND HEALTH SCIENCES  -- Clinical Medicine -- Cardiac and Cardiovascular Systems (hsv//eng)
MEDICIN OCH HÄLSOVETENSKAP  -- Hälsovetenskap -- Folkhälsovetenskap, global hälsa, socialmedicin och epidemiologi (hsv//swe)
MEDICAL AND HEALTH SCIENCES  -- Health Sciences -- Public Health, Global Health, Social Medicine and Epidemiology (hsv//eng)

Nyckelord

CTEPH
risk stratification
survival
pulmonary endarterectomy
goal-oriented treatment
CTEPH
goal-oriented treatment
pulmonary endarterectomy
risk stratification
survival
survival.

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