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  • Bothou, ChristinaKlinik für Endokrinologie, Diabetologie und Klinische Ernährung, Universitätsspital Zürich, Zürich, Switzerland,Univ Spital Zurich, Switzerland (författare)

Current Management and Outcome of Pregnancies in Women With Adrenal Insufficiency : Experience from a Multicenter Survey

  • Artikel/kapitelEngelska2020

Förlag, utgivningsår, omfång ...

  • 2020-05-19
  • Oxford University Press,2020
  • printrdacarrier

Nummerbeteckningar

  • LIBRIS-ID:oai:DiVA.org:oru-108834
  • https://urn.kb.se/resolve?urn=urn:nbn:se:oru:diva-108834URI
  • https://doi.org/10.1210/clinem/dgaa266DOI
  • https://urn.kb.se/resolve?urn=urn:nbn:se:liu:diva-170003URI
  • http://kipublications.ki.se/Default.aspx?queryparsed=id:144575464URI
  • https://gup.ub.gu.se/publication/297312URI

Kompletterande språkuppgifter

  • Språk:engelska
  • Sammanfattning på:engelska

Ingår i deldatabas

Klassifikation

  • Ämneskategori:ref swepub-contenttype
  • Ämneskategori:art swepub-publicationtype

Anmärkningar

  • Funding Agencies:James A. Ruppe Career Development Award in EndocrinologyCatalyst Award for Advancing in Academics from Mayo Clinic
  • Funding Agencies|Deutsche Forschungsgemeinschaft (DFG)German Research Foundation (DFG) [CRC/Transregio 205/1]; James A. Ruppe Career Development Award in Endocrinology; Catalyst Award for Advancing in Academics from Mayo Clinic; National Institute of Diabetes and Digestive and Kidney Diseases (NIDDK) of the National Institutes of Health (NIH) USA [K23DK121888]
  • Context: Appropriate management of adrenal insufficiency (AI) in pregnancy can be challenging due to the rarity of the disease and lack of evidence-based recommendations to guide glucocorticoid and mineralocorticoid dosage adjustment.Objective: Multicenter survey on current clinical approaches in managing AI during pregnancy.Design: Retrospective anonymized data collection from 19 international centers from 2013 to 2019.Setting and patients: 128 pregnancies in 113 women with different causes of AI: Addison disease (44%), secondary AI (25%), congenital adrenal hyperplasia (25%), and acquired AI due to bilateral adrenalectomy (6%).Results: Hydrocortisone (HC) was the most commonly used glucocorticoid in 83% (97/117) of pregnancies. Glucocorticoid dosage was increased at any time during pregnancy in 73/128 (57%) of cases. In these cases, the difference in the daily dose of HC equivalent between baseline and the third trimester was 8.6 ± 5.4 (range 1-30) mg. Fludrocortisone dosage was increased in fewer cases (7/54 during the first trimester, 9/64 during the second trimester, and 9/62 cases during the third trimester). Overall, an adrenal crisis was reported in 9/128 (7%) pregnancies. Cesarean section was the most frequent mode of delivery at 58% (69/118). Fetal complications were reported in 3/120 (3%) and minor maternal complications in 15/120 (13%) pregnancies without fatal outcomes.Conclusions: This survey confirms good maternal and fetal outcome in women with AI managed in specialized endocrine centers. An emphasis on careful endocrine follow-up and repeated patient education is likely to have reduced the risk of adrenal crisis and resulted in positive outcomes.

Ämnesord och genrebeteckningar

Biuppslag (personer, institutioner, konferenser, titlar ...)

  • Anand, GurpreetKlinik für Endokrinologie, Diabetologie und Klinische Ernährung, Universitätsspital Zürich, Zürich, Switzerland,Univ Spital Zurich, Switzerland (författare)
  • Li, DingfengDivision of Endocrinology, Diabetes, Metabolism and Nutrition, Mayo Clinic, Rochester, Minnesota, USA,Mayo Clin, MN 55905 USA (författare)
  • Kienitz, TinaEndocrinology in Charlottenburg, Berlin, Germany,Endocrinol Charlottenburg, Germany (författare)
  • Seejore, KhyatishaDepartment of Endocrinology, Leeds Teaching Hospitals NHS Trust, St James’s University Hospital, Leeds, England,St James Univ Hosp, England (författare)
  • Simeoli, ChiaraDipartimento di Medicina Clinica e Chirurgia, Sezione di Endocrinologia, Università Federico II di Napoli, Naples, Italy,Univ Federico II Napoli, Italy (författare)
  • Ebbehoj, AndreasDepartment of Clinical Medicine, Department of Endocrinology and Diabetes, Aarhus University, Aarhus, Denmark,Aarhus Univ, Denmark (författare)
  • Ward, Emma G.Department of Endocrinology, Leeds Teaching Hospitals NHS Trust, St James’s University Hospital, Leeds, England,St James Univ Hosp, England (författare)
  • Paragliola, Rosa MariaUnit of Endocrinology, Università Cattolica del Sacro Cuore – Fondazione Policlinico Universitario Agostino Gemelli IRCCS, Rome, Italy,Univ Cattolica Sacro Cuore Fdn Policlin Univ Agos, Italy (författare)
  • Ferrigno, RosarioDipartimento di Medicina Clinica e Chirurgia, Sezione di Endocrinologia, Università Federico II di Napoli, Naples, Italy,Univ Federico II Napoli, Italy (författare)
  • Badenhoop, KlausDepartment of Internal Medicine I, Division of Endocrinology, Diabetes and Metabolism, University Hospital, Frankfurt, Germany,Univ Hosp, Frankfurt, Germany (författare)
  • Bensing, SophieKarolinska Institutet (författare)
  • Oksnes, MarianneEndocrinology in Charlottenburg, Berlin, Germany; Department of Clinical Science and K.G. Jebsen Center for Autoimmune Disorders, University of Bergen, Jonas Liesvei, Bergen, Norway,Endocrinol Charlottenburg, Germany; Univ Bergen, Norway; Univ Bergen, Norway (författare)
  • Esposito, DanielaGothenburg University,Göteborgs universitet,Institutionen för medicin, avdelningen för invärtesmedicin och klinisk nutrition,Institute of Medicine, Department of Internal Medicine and Clinical Nutrition(Swepub:gu)xespda (författare)
  • Bergthorsdottir, Ragnhildur,1971Gothenburg University,Göteborgs universitet,Institutionen för medicin, avdelningen för invärtesmedicin och klinisk nutrition,Institute of Medicine, Department of Internal Medicine and Clinical Nutrition(Swepub:gu)xberag (författare)
  • Drake, WilliamDepartment of Endocrinology, St Bartholomew’s Hospital, London, UK,St Bartholomews Hosp, England (författare)
  • Wahlberg, Jeanette,1969-Linköpings universitet,Avdelningen för diagnostik och specialistmedicin,Medicinska fakulteten,Region Östergötland, Endokrinmedicinska kliniken(Swepub:liu)jeawa98 (författare)
  • Reisch, NicoleDepartment of Endocrinology, Medizinische Klinik und Poliklinik IV, Klinikum der Universität München, Munich, Germany (författare)
  • Hahner, StefanieDepartment of Internal Medicine I, Endocrinology and Diabetes Unit, University Hospital of Würzburg, University of Würzburg, Germany (författare)
  • Pearce, SimonTranslational and Clinical Research Institute, Newcastle University, Newcastle upon Tyne, UK,Newcastle Univ, England (författare)
  • Trainer, PeterThe Christie NHS Foundation, MAHSC, Wilmslow Road, Manchester, England,Christie NHS Fdn, England (författare)
  • Etzrodt-Walter, GwendolinPraxis Dr. Etzrodt-Walter Endokrinologiezentrum Ulm, Ulm, Germany,Praxis Dr Etzrodt Walter Endokrinol Zentrum Ulm, Germany (författare)
  • Thalmann, Sébastien P.Ärztezentrum Sihlcity, Zurich, Switzerland (författare)
  • Sævik, Åse B.Department of Clinical Science and K.G. Jebsen Center for Autoimmune Disorders, University of Bergen, Jonas Liesvei, Bergen, Norway,Univ Bergen, Norway (författare)
  • Husebye, EysteinDepartment of Clinical Science and K.G. Jebsen Center for Autoimmune Disorders, University of Bergen, Jonas Liesvei, Bergen, Norway,Univ Bergen, Norway (författare)
  • Isidori, Andrea M.Department of Experimental Medicine, Sapienza University of Rome, Rome, Italy,Sapienza Univ Rome, Italy (författare)
  • Falhammar, HenrikKarolinska Institutet (författare)
  • Meyer, GesineDepartment of Internal Medicine I, Division of Endocrinology, Diabetes and Metabolism, University Hospital, Frankfurt, Germany,Univ Hosp, Germany (författare)
  • Corsello, Salvatore M.Unit of Endocrinology, Università Cattolica del Sacro Cuore – Fondazione Policlinico Universitario Agostino Gemelli IRCCS, Rome, Italy,Univ Cattolica Sacro Cuore Fdn Policlin Univ Agos, Italy (författare)
  • Pivonello, RosarioDipartimento di Medicina Clinica e Chirurgia, Sezione di Endocrinologia, Università Federico II di Napoli, Naples, Italy,Univ Federico II Napoli, Italy (författare)
  • Murray, RobertDepartment of Endocrinology, Leeds Teaching Hospitals NHS Trust, St James’s University Hospital, Leeds, England,St James Univ Hosp, England (författare)
  • Bancos, IrinaDivision of Endocrinology, Diabetes, Metabolism and Nutrition, Mayo Clinic, Rochester, Minnesota, USA,Mayo Clin, MN 55905 USA (författare)
  • Quinkler, MarcusEndocrinology in Charlottenburg, Berlin, Germany,Endocrinol Charlottenburg, Germany (författare)
  • Beuschlein, FelixKlinik für Endokrinologie, Diabetologie und Klinische Ernährung, Universitätsspital Zürich, Zürich, Switzerland; Department of Endocrinology, Medizinische Klinik und Poliklinik IV, Klinikum der Universität München, Munich, Germany,Univ Spital Zurich, Switzerland; Klinikum Univ Munchen, Germany (författare)
  • Klinik für Endokrinologie, Diabetologie und Klinische Ernährung, Universitätsspital Zürich, Zürich, SwitzerlandUniv Spital Zurich, Switzerland (creator_code:org_t)

Sammanhörande titlar

  • Ingår i:Journal of Clinical Endocrinology and Metabolism: Oxford University Press105:80021-972X1945-7197

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