Search: onr:"swepub:oai:DiVA.org:oru-6968" >
Budd-Chiari syndrom...
-
Rajani, RupeshLinköpings universitet,Gastroenterologi och hepatologi,Hälsouniversitetet
(author)
Budd-Chiari syndrome in Sweden : epidemiology, clinical characteristics and survival - an 18-year experience
- Article/chapterEnglish2009
Publisher, publication year, extent ...
-
Oxford :Blackwell Munksgaard,2009
-
printrdacarrier
Numbers
-
LIBRIS-ID:oai:DiVA.org:oru-6968
-
https://urn.kb.se/resolve?urn=urn:nbn:se:oru:diva-6968URI
-
https://doi.org/10.1111/j.1478-3231.2008.01838.xDOI
-
https://lup.lub.lu.se/record/1313311URI
-
https://urn.kb.se/resolve?urn=urn:nbn:se:uu:diva-153473URI
-
https://urn.kb.se/resolve?urn=urn:nbn:se:liu:diva-16408URI
Supplementary language notes
-
Language:English
-
Summary in:English
Part of subdatabase
Classification
-
Subject category:ref swepub-contenttype
-
Subject category:art swepub-publicationtype
Notes
-
BACKGROUND: The exact incidence and prevalence of Budd-Chiari syndrome (BCS) is unknown in the general population. Published reports differ in terms of the clinical characteristics, effects of therapy and survival. AIMS: To investigate the epidemiology, clinical presentation and survival in patients with BCS. METHODS: Retrospective multicentre study in Sweden reviewing the medical records of all patients with BCS 1986-2003, identified from the computerised diagnosis database of 11 hospitals, including all university hospitals and liver transplantation centres. RESULTS: Forty-three patients with BCS were identified, of whom nine (21%) had concomitant portal vein thrombosis. The mean age-standardised incidence and prevalence rates in 1990-2001 were calculated to be 0.8 per million per year and 1.4 per million inhabitants respectively. Myeloproliferative disorders (38%), thrombophilic factors (31%) and oral contraceptives (30%) were common aetiological factors. Two or more risk factors were present in 44%. In 23%, no risk factor was evident. The median follow-up time was 2.7 years. Seventy-two percent were on anticoagulant therapy during follow-up. Transjugular intrahepatic portosystemic shunting, surgical shunting procedures and liver transplantation were performed in 4, 6 and 18 patients respectively. Nineteen patients died. The overall transplantation-free survival at 1, 5 and 10 years was 47, 28 and 17% respectively. CONCLUSIONS: Budd-Chiari syndrome is a rare disorder; the mean age-standardised incidence and prevalence rates in Sweden in 1990-2001 were calculated to be 0.8 per million per year and 1.4 per million inhabitants respectively. The presence of a myeloproliferative disorder was a common aetiological factor in our cohort and about half of the patients had a multifactorial aetiology. The transplantation-free survival was poor.
Subject headings and genre
Added entries (persons, corporate bodies, meetings, titles ...)
-
Melin, TorUniversity Hospital, Lund
(author)
-
Björnsson, EinarSahlgrenska University Hospital, Göteborg
(author)
-
Broomé, UlrikaKarolinska University Hospital, Stockholm
(author)
-
Sangfelt, PerUniversity Uppsala Hospital, Uppsala
(author)
-
Danielsson, ÅkeUmea University Hospital, Umeå
(author)
-
Gustavsson, AndersÖrebro universitet,Hälsoakademin,University Hospital, Örebro(Swepub:oru)argn
(author)
-
Grip, OlofLund University,Lunds universitet,Enheten för kroniska inflammatoriska och degenerativa sjukdomar,Forskargrupper vid Lunds universitet,Chronic Inflammatory and Degenerative Diseases Research Unit,Lund University Research Groups,Malmö University Hospital, Malmö(Swepub:lu)medf-ogr
(author)
-
Svensson, HansVrinnevi Hospital, Norrköping
(author)
-
Lööf, LarsUppsala universitet,Centrum för klinisk forskning, Västerås,Västerås City Hospital, Västerås(Swepub:uu)larsloof
(author)
-
Wallerstedt, SvenÖstra Hospital, Gothenberg
(author)
-
Almer, SvenÖstergötlands Läns Landsting,Linköpings universitet,Gastroenterologi och hepatologi,Hälsouniversitetet,Endokrin- och magtarmmedicinska kliniken US(Swepub:liu)sveal38
(author)
-
Linköpings universitetGastroenterologi och hepatologi
(creator_code:org_t)
Related titles
-
In:Liver international (Print)Oxford : Blackwell Munksgaard29:2, s. 253-2591478-32231478-3231
Internet link
Find in a library
To the university's database
- By the author/editor
-
Rajani, Rupesh
-
Melin, Tor
-
Björnsson, Einar
-
Broomé, Ulrika
-
Sangfelt, Per
-
Danielsson, Åke
-
show more...
-
Gustavsson, Ande ...
-
Grip, Olof
-
Svensson, Hans
-
Lööf, Lars
-
Wallerstedt, Sve ...
-
Almer, Sven
-
show less...
- About the subject
-
- MEDICAL AND HEALTH SCIENCES
-
MEDICAL AND HEAL ...
-
and Clinical Medicin ...
-
and Gastroenterology ...
-
- MEDICAL AND HEALTH SCIENCES
-
MEDICAL AND HEAL ...
-
and Clinical Medicin ...
-
and Rheumatology and ...
- Articles in the publication
-
Liver internatio ...
- By the university
-
Örebro University
-
Lund University
-
Uppsala University
-
Linköping University