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Practices in prescr...
Practices in prescribing protein substitutes for PKU in Europe : No uniformity of approach
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Aguiar, A. (author)
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Ahring, K. (author)
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Almeida, M. F. (author)
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show more...
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Assoun, M. (author)
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Belanger Quintana, A. (author)
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Bigot, S. (author)
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Bihet, G. (author)
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- Malmberg, Karin Blom (author)
- Uppsala universitet,Institutionen för kostvetenskap
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Burlina, A. (author)
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Bushueva, T. (author)
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Caris, A. (author)
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Chan, H. (author)
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Clark, A. (author)
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Clark, S. (author)
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Cochrane, B. (author)
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Corthouts, K. (author)
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Dalmau, J. (author)
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Dassy, M. (author)
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De Meyer, A. (author)
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Didycz, B. (author)
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Diels, M. (author)
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Dokupil, K. (author)
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Dubois, S. (author)
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Eftring, K. (author)
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Ekengren, J. (author)
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Ellerton, C. (author)
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Evans, S. (author)
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Faria, A. (author)
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Fischer, A. (author)
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Ford, S. (author)
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Freisinger, P. (author)
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Gizewska, M. (author)
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Gokmen-Ozel, H. (author)
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Gribben, J. (author)
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Gunden, F. (author)
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Heddrich-Ellerbrok, M. (author)
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Heiber, S. (author)
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Heidenborg, C. (author)
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Jankowski, C. (author)
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Janssen-Regelink, R. (author)
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Jones, I. (author)
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Jonkers, C. (author)
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Joerg-Streller, M. (author)
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Kaalund-Hansen, K. (author)
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Kiss, E. (author)
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Lammardo, A. M. (author)
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Lang, K. (author)
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Lier, D. (author)
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Lilje, R. (author)
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Lowry, S. (author)
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Luyten, K. (author)
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MacDonald, A. (author)
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Meyer, U. (author)
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Moor, D. (author)
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Pal, A. (author)
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Robert, M. (author)
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Robertson, L. (author)
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Rocha, J. C. (author)
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Rohde, C. (author)
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Ross, K. (author)
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Saruhan, S. (author)
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Sjoqvist, E. (author)
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Skeath, R. (author)
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Stoelen, L. (author)
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Ter Horst, N. M. (author)
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Terry, A. (author)
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Timmer, C. (author)
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Tuncer, N. (author)
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Vande Kerckhove, K. (author)
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van der Ploeg, L. (author)
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van Rijn, M. (author)
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van Spronsen, F. J. (author)
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van Teeffelen-Heithoff, A. (author)
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van Wegberg, A. (author)
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van Wyk, K. (author)
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Vasconcelos, C. (author)
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Vitoria, I. (author)
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Wildgoose, J. (author)
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Webster, D. (author)
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White, F. J. (author)
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Zweers, H. (author)
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(creator_code:org_t)
- Elsevier BV, 2015
- 2015
- English.
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In: Molecular Genetics and Metabolism. - : Elsevier BV. - 1096-7192 .- 1096-7206. ; 115:1, s. 17-22
- Related links:
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https://urn.kb.se/re...
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https://doi.org/10.1...
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Abstract
Subject headings
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- Background: There appears little consensus concerning protein requirements in phenylketonuria (PKU). Methods: A questionnaire completed by 63 European and Turkish IMD centres from 18 countries collected data on prescribed total protein intake (natural/intact protein and phenylalanine-free protein substitute [PS]) by age, administration frequency and method, monitoring, and type of protein substitute. Data were analysed by European region using descriptive statistics. Results: The amount of total protein (from PS and natural/intact protein) varied according to the European region. Higher median amounts of total protein were prescribed in infants and children in Northern Europe (n = 24 centres) (infants <1 year, >2-3 g/kg/day; 1-3 years of age, >2-3 g/kg/day; 4-10 years of age, >1.5-2.5 g/kg/day) and Southern Europe (n = 10 centres) (infants <1 year, 2.5 g/kg/day, 1-3 years of age, 2 g/kg/day; 4-10 years of age, 1.5-2 g/kg/day), than by Eastern Europe (n = 4 centres) (infants <1 year, 2.5 g/kg/day, 1-3 years of age, >2-2.5 g/kg/day; 4-10 years of age, >1.5-2 g/kg/day) and with Western Europe (n = 25 centres) giving the least (infants <1 year, >2-2.5 g/kg/day, 1-3 years of age, 1.5-2 g/kg/day; 4-10 years of age, 1-1.5 g/kg/day). Total protein prescription was similar in patients aged >10 years (1-1.5 g/kg/day) and maternal patients (1-1.5 g/kg/day). Conclusions: The amounts of total protein prescribed varied between European countries and appeared to be influenced by geographical region. In PKU, all gave higher than the recommended 2007 WHO/FAO/UNU safe levels of protein intake for the general population.
Subject headings
- MEDICIN OCH HÄLSOVETENSKAP -- Hälsovetenskap -- Annan hälsovetenskap (hsv//swe)
- MEDICAL AND HEALTH SCIENCES -- Health Sciences -- Other Health Sciences (hsv//eng)
Keyword
- Phenylketonuria
- Protein substitute
- L-Amino acid supplements
- Glycomacropeptide
Publication and Content Type
- ref (subject category)
- art (subject category)
Find in a library
To the university's database
- By the author/editor
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Aguiar, A.
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Ahring, K.
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Almeida, M. F.
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Assoun, M.
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Belanger Quintan ...
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Bigot, S.
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show more...
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Bihet, G.
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Malmberg, Karin ...
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Burlina, A.
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Bushueva, T.
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Caris, A.
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Chan, H.
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Clark, A.
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Clark, S.
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Cochrane, B.
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Corthouts, K.
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Dalmau, J.
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Dassy, M.
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De Meyer, A.
-
Didycz, B.
-
Diels, M.
-
Dokupil, K.
-
Dubois, S.
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Eftring, K.
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Ekengren, J.
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Ellerton, C.
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Evans, S.
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Faria, A.
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Fischer, A.
-
Ford, S.
-
Freisinger, P.
-
Gizewska, M.
-
Gokmen-Ozel, H.
-
Gribben, J.
-
Gunden, F.
-
Heddrich-Ellerbr ...
-
Heiber, S.
-
Heidenborg, C.
-
Jankowski, C.
-
Janssen-Regelink ...
-
Jones, I.
-
Jonkers, C.
-
Joerg-Streller, ...
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Kaalund-Hansen, ...
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Kiss, E.
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Lammardo, A. M.
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Lang, K.
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Lier, D.
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Lilje, R.
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Lowry, S.
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Luyten, K.
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MacDonald, A.
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Meyer, U.
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Moor, D.
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Pal, A.
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Robert, M.
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Robertson, L.
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Rocha, J. C.
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Rohde, C.
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Ross, K.
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Saruhan, S.
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Sjoqvist, E.
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Skeath, R.
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Stoelen, L.
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Ter Horst, N. M.
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Terry, A.
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Timmer, C.
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Tuncer, N.
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Vande Kerckhove, ...
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van der Ploeg, L ...
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van Rijn, M.
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van Spronsen, F. ...
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van Teeffelen-He ...
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van Wegberg, A.
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van Wyk, K.
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Vasconcelos, C.
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Vitoria, I.
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Wildgoose, J.
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Webster, D.
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White, F. J.
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Zweers, H.
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- About the subject
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- MEDICAL AND HEALTH SCIENCES
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MEDICAL AND HEAL ...
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and Health Sciences
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and Other Health Sci ...
- Articles in the publication
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Molecular Geneti ...
- By the university
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Uppsala University