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IgA vasculitis neph...
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Stanway, JamesRoyal Free Hosp, England
(författare)
IgA vasculitis nephritis-outcomes in adult-onset disease
- Artikel/kapitelEngelska2024
Förlag, utgivningsår, omfång ...
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2024
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OXFORD UNIV PRESS,2024
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printrdacarrier
Nummerbeteckningar
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LIBRIS-ID:oai:DiVA.org:liu-200959
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https://urn.kb.se/resolve?urn=urn:nbn:se:liu:diva-200959URI
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https://doi.org/10.1093/rheumatology/keae030DOI
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Språk:engelska
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Sammanfattning på:engelska
Ingår i deldatabas
Klassifikation
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Ämneskategori:ref swepub-contenttype
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Ämneskategori:art swepub-publicationtype
Anmärkningar
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Objectives: IgA vasculitis (IgAV) in adults has been relatively under-investigated. Since outcomes are worse in other forms of vasculitis with increasing age, we investigated the outcomes of IgAV comparing younger adults (18-34), middle-aged adults (35-64) and elderly patients (>= 64 years) focusing on kidney outcomes. Methods: We identified patients with renal biopsy-confirmed IgAV nephritis and collected data regarding clinical features and progression to end stage kidney disease (ESKD). The relationship between patient factors and ESKD was analysed by regression. Results: We identified 202 cases, 34% aged 18-34, 43% aged 35-64 and 23% elderly (>64 years). Median follow-up was 44 months. Elderly patients were more likely to present with ESKD (23.9%) compared with middle-aged (13.7%) and younger adults (2.9%) (chi(2 )11.6, P = 0.002). In patients with independent kidney function at biopsy, there was no difference in outcomes between age groups. Male gender, Black ethnicity, diabetes, histological evidence of chronic renal damage and estimated glomerular filtration rate < 30 ml/min were risk factors for development of ESKD. In this observational study 68.3% of patients received glucocorticoids and 56.9% additional immunosuppression. Conclusion: Elderly patients with IgAV are more likely to have ESKD at presentation, but there is no difference in renal survival between age groups, among those presenting with independent renal function. Renal impairment at biopsy is an independent risk factor for subsequent development of ESKD. There is significant variability in the timing of kidney biopsy and management of these patients among specialist centres. Young adults have outcomes more in keeping with childhood IgAV.
Ämnesord och genrebeteckningar
Biuppslag (personer, institutioner, konferenser, titlar ...)
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Brown, NinaSalford Royal Fdn Trust, England
(författare)
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Pervez, AfeeraQueen Elizabeth Hosp, England
(författare)
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van de Perre, ElsAddenbrookes Hosp, England
(författare)
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Tollitt, JamesSalford Royal Fdn Trust, England
(författare)
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Marketos, Nikolaos,1976-Linköpings universitet,Avdelningen för diagnostik och specialistmedicin,Medicinska fakulteten(Swepub:liu)nikma29
(författare)
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Wong, NikkiImperial Coll London, England
(författare)
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Dhaygude, AjayRoyal Preston Hosp, England
(författare)
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Ponnusamy, ArvindRoyal Preston Hosp, England
(författare)
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O'Riordan, EdSalford Royal Fdn Trust, England
(författare)
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Venning, MichaelManchester Royal Infirm, England
(författare)
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Segelmark, MartenLund Univ, Sweden
(författare)
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Morgan, MatthewQueen Elizabeth Hosp, England
(författare)
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Jayne, DavidAddenbrookes Hosp, England
(författare)
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Hamilton, PatrickManchester Royal Infirm, England
(författare)
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Pusey, Charles D.Imperial Coll London, England
(författare)
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Oni, LouiseAlder Hey Childrens NHS Fdn Trust Hosp, England
(författare)
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Salama, Alan D.Royal Free Hosp, England
(författare)
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Royal Free Hosp, EnglandSalford Royal Fdn Trust, England
(creator_code:org_t)
Sammanhörande titlar
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Ingår i:Rheumatology: OXFORD UNIV PRESS1462-03241462-0332
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Till lärosätets databas
- Av författaren/redakt...
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Stanway, James
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Brown, Nina
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Pervez, Afeera
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van de Perre, El ...
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Tollitt, James
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Marketos, Nikola ...
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visa fler...
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Wong, Nikki
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Dhaygude, Ajay
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Ponnusamy, Arvin ...
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O'Riordan, Ed
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Venning, Michael
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Segelmark, Marte ...
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Morgan, Matthew
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Jayne, David
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Hamilton, Patric ...
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Pusey, Charles D ...
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Oni, Louise
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Salama, Alan D.
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visa färre...
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- MEDICIN OCH HÄLSOVETENSKAP
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MEDICIN OCH HÄLS ...
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och Klinisk medicin
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och Odontologi
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Rheumatology
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Linköpings universitet