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Sökning: id:"swepub:oai:DiVA.org:oru-6968" > Budd-Chiari syndrom...

  • Rajani, RupeshLinköpings universitet,Gastroenterologi och hepatologi,Hälsouniversitetet (författare)

Budd-Chiari syndrome in Sweden : epidemiology, clinical characteristics and survival - an 18-year experience

  • Artikel/kapitelEngelska2009

Förlag, utgivningsår, omfång ...

  • Oxford :Blackwell Munksgaard,2009
  • printrdacarrier

Nummerbeteckningar

  • LIBRIS-ID:oai:DiVA.org:oru-6968
  • https://urn.kb.se/resolve?urn=urn:nbn:se:oru:diva-6968URI
  • https://doi.org/10.1111/j.1478-3231.2008.01838.xDOI
  • https://lup.lub.lu.se/record/1313311URI
  • https://urn.kb.se/resolve?urn=urn:nbn:se:uu:diva-153473URI
  • https://urn.kb.se/resolve?urn=urn:nbn:se:liu:diva-16408URI

Kompletterande språkuppgifter

  • Språk:engelska
  • Sammanfattning på:engelska

Ingår i deldatabas

Klassifikation

  • Ämneskategori:ref swepub-contenttype
  • Ämneskategori:art swepub-publicationtype

Anmärkningar

  • BACKGROUND: The exact incidence and prevalence of Budd-Chiari syndrome (BCS) is unknown in the general population. Published reports differ in terms of the clinical characteristics, effects of therapy and survival. AIMS: To investigate the epidemiology, clinical presentation and survival in patients with BCS. METHODS: Retrospective multicentre study in Sweden reviewing the medical records of all patients with BCS 1986-2003, identified from the computerised diagnosis database of 11 hospitals, including all university hospitals and liver transplantation centres. RESULTS: Forty-three patients with BCS were identified, of whom nine (21%) had concomitant portal vein thrombosis. The mean age-standardised incidence and prevalence rates in 1990-2001 were calculated to be 0.8 per million per year and 1.4 per million inhabitants respectively. Myeloproliferative disorders (38%), thrombophilic factors (31%) and oral contraceptives (30%) were common aetiological factors. Two or more risk factors were present in 44%. In 23%, no risk factor was evident. The median follow-up time was 2.7 years. Seventy-two percent were on anticoagulant therapy during follow-up. Transjugular intrahepatic portosystemic shunting, surgical shunting procedures and liver transplantation were performed in 4, 6 and 18 patients respectively. Nineteen patients died. The overall transplantation-free survival at 1, 5 and 10 years was 47, 28 and 17% respectively. CONCLUSIONS: Budd-Chiari syndrome is a rare disorder; the mean age-standardised incidence and prevalence rates in Sweden in 1990-2001 were calculated to be 0.8 per million per year and 1.4 per million inhabitants respectively. The presence of a myeloproliferative disorder was a common aetiological factor in our cohort and about half of the patients had a multifactorial aetiology. The transplantation-free survival was poor.

Ämnesord och genrebeteckningar

Biuppslag (personer, institutioner, konferenser, titlar ...)

  • Melin, TorUniversity Hospital, Lund (författare)
  • Björnsson, EinarSahlgrenska University Hospital, Göteborg (författare)
  • Broomé, UlrikaKarolinska University Hospital, Stockholm (författare)
  • Sangfelt, PerUniversity Uppsala Hospital, Uppsala (författare)
  • Danielsson, ÅkeUmea University Hospital, Umeå (författare)
  • Gustavsson, AndersÖrebro universitet,Hälsoakademin,University Hospital, Örebro(Swepub:oru)argn (författare)
  • Grip, OlofLund University,Lunds universitet,Enheten för kroniska inflammatoriska och degenerativa sjukdomar,Forskargrupper vid Lunds universitet,Chronic Inflammatory and Degenerative Diseases Research Unit,Lund University Research Groups,Malmö University Hospital, Malmö(Swepub:lu)medf-ogr (författare)
  • Svensson, HansVrinnevi Hospital, Norrköping (författare)
  • Lööf, LarsUppsala universitet,Centrum för klinisk forskning, Västerås,Västerås City Hospital, Västerås(Swepub:uu)larsloof (författare)
  • Wallerstedt, SvenÖstra Hospital, Gothenberg (författare)
  • Almer, SvenÖstergötlands Läns Landsting,Linköpings universitet,Gastroenterologi och hepatologi,Hälsouniversitetet,Endokrin- och magtarmmedicinska kliniken US(Swepub:liu)sveal38 (författare)
  • Linköpings universitetGastroenterologi och hepatologi (creator_code:org_t)

Sammanhörande titlar

  • Ingår i:Liver international (Print)Oxford : Blackwell Munksgaard29:2, s. 253-2591478-32231478-3231

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