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Budd-Chiari syndrom...
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Rajani, RupeshLinköpings universitet,Gastroenterologi och hepatologi,Hälsouniversitetet
(författare)
Budd-Chiari syndrome in Sweden : epidemiology, clinical characteristics and survival - an 18-year experience
- Artikel/kapitelEngelska2009
Förlag, utgivningsår, omfång ...
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Oxford :Blackwell Munksgaard,2009
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printrdacarrier
Nummerbeteckningar
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LIBRIS-ID:oai:DiVA.org:oru-6968
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https://urn.kb.se/resolve?urn=urn:nbn:se:oru:diva-6968URI
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https://doi.org/10.1111/j.1478-3231.2008.01838.xDOI
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https://lup.lub.lu.se/record/1313311URI
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https://urn.kb.se/resolve?urn=urn:nbn:se:uu:diva-153473URI
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https://urn.kb.se/resolve?urn=urn:nbn:se:liu:diva-16408URI
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Språk:engelska
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Sammanfattning på:engelska
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Ämneskategori:ref swepub-contenttype
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Ämneskategori:art swepub-publicationtype
Anmärkningar
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BACKGROUND: The exact incidence and prevalence of Budd-Chiari syndrome (BCS) is unknown in the general population. Published reports differ in terms of the clinical characteristics, effects of therapy and survival. AIMS: To investigate the epidemiology, clinical presentation and survival in patients with BCS. METHODS: Retrospective multicentre study in Sweden reviewing the medical records of all patients with BCS 1986-2003, identified from the computerised diagnosis database of 11 hospitals, including all university hospitals and liver transplantation centres. RESULTS: Forty-three patients with BCS were identified, of whom nine (21%) had concomitant portal vein thrombosis. The mean age-standardised incidence and prevalence rates in 1990-2001 were calculated to be 0.8 per million per year and 1.4 per million inhabitants respectively. Myeloproliferative disorders (38%), thrombophilic factors (31%) and oral contraceptives (30%) were common aetiological factors. Two or more risk factors were present in 44%. In 23%, no risk factor was evident. The median follow-up time was 2.7 years. Seventy-two percent were on anticoagulant therapy during follow-up. Transjugular intrahepatic portosystemic shunting, surgical shunting procedures and liver transplantation were performed in 4, 6 and 18 patients respectively. Nineteen patients died. The overall transplantation-free survival at 1, 5 and 10 years was 47, 28 and 17% respectively. CONCLUSIONS: Budd-Chiari syndrome is a rare disorder; the mean age-standardised incidence and prevalence rates in Sweden in 1990-2001 were calculated to be 0.8 per million per year and 1.4 per million inhabitants respectively. The presence of a myeloproliferative disorder was a common aetiological factor in our cohort and about half of the patients had a multifactorial aetiology. The transplantation-free survival was poor.
Ämnesord och genrebeteckningar
Biuppslag (personer, institutioner, konferenser, titlar ...)
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Melin, TorUniversity Hospital, Lund
(författare)
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Björnsson, EinarSahlgrenska University Hospital, Göteborg
(författare)
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Broomé, UlrikaKarolinska University Hospital, Stockholm
(författare)
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Sangfelt, PerUniversity Uppsala Hospital, Uppsala
(författare)
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Danielsson, ÅkeUmea University Hospital, Umeå
(författare)
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Gustavsson, AndersÖrebro universitet,Hälsoakademin,University Hospital, Örebro(Swepub:oru)argn
(författare)
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Grip, OlofLund University,Lunds universitet,Enheten för kroniska inflammatoriska och degenerativa sjukdomar,Forskargrupper vid Lunds universitet,Chronic Inflammatory and Degenerative Diseases Research Unit,Lund University Research Groups,Malmö University Hospital, Malmö(Swepub:lu)medf-ogr
(författare)
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Svensson, HansVrinnevi Hospital, Norrköping
(författare)
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Lööf, LarsUppsala universitet,Centrum för klinisk forskning, Västerås,Västerås City Hospital, Västerås(Swepub:uu)larsloof
(författare)
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Wallerstedt, SvenÖstra Hospital, Gothenberg
(författare)
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Almer, SvenÖstergötlands Läns Landsting,Linköpings universitet,Gastroenterologi och hepatologi,Hälsouniversitetet,Endokrin- och magtarmmedicinska kliniken US(Swepub:liu)sveal38
(författare)
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Linköpings universitetGastroenterologi och hepatologi
(creator_code:org_t)
Sammanhörande titlar
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Ingår i:Liver international (Print)Oxford : Blackwell Munksgaard29:2, s. 253-2591478-32231478-3231
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Rajani, Rupesh
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Melin, Tor
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Björnsson, Einar
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Broomé, Ulrika
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Sangfelt, Per
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Danielsson, Åke
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visa fler...
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Gustavsson, Ande ...
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Grip, Olof
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Svensson, Hans
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Lööf, Lars
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Wallerstedt, Sve ...
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Almer, Sven
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- MEDICIN OCH HÄLSOVETENSKAP
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och Klinisk medicin
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och Gastroenterologi
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och Reumatologi och ...
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Örebro universitet
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