Practices in prescribing protein substitutes for PKU in Europe: No uniformity of approach

↓ Direkt till sidans innehåll
↓ Direkt till sidans sekundära innehåll (sidomenyn)

Search: WFRF:(Bigot M) > (2015-2019) > Practices in prescr...

Details
MARC

Aguiar, A. (author)

Practices in prescribing protein substitutes for PKU in Europe : No uniformity of approach

Article/chapterEnglish2015

Publisher, publication year, extent ...

Elsevier BV,2015
printrdacarrier

Numbers

LIBRIS-ID:oai:DiVA.org:uu-256539
https://urn.kb.se/resolve?urn=urn:nbn:se:uu:diva-256539URI
https://doi.org/10.1016/j.ymgme.2015.03.006DOI

Supplementary language notes

Language:English
Summary in:English

Part of subdatabase

SwePubSwePub

Classification

Subject category:ref swepub-contenttype
Subject category:art swepub-publicationtype

Notes

Background: There appears little consensus concerning protein requirements in phenylketonuria (PKU). Methods: A questionnaire completed by 63 European and Turkish IMD centres from 18 countries collected data on prescribed total protein intake (natural/intact protein and phenylalanine-free protein substitute [PS]) by age, administration frequency and method, monitoring, and type of protein substitute. Data were analysed by European region using descriptive statistics. Results: The amount of total protein (from PS and natural/intact protein) varied according to the European region. Higher median amounts of total protein were prescribed in infants and children in Northern Europe (n = 24 centres) (infants <1 year, >2-3 g/kg/day; 1-3 years of age, >2-3 g/kg/day; 4-10 years of age, >1.5-2.5 g/kg/day) and Southern Europe (n = 10 centres) (infants <1 year, 2.5 g/kg/day, 1-3 years of age, 2 g/kg/day; 4-10 years of age, 1.5-2 g/kg/day), than by Eastern Europe (n = 4 centres) (infants <1 year, 2.5 g/kg/day, 1-3 years of age, >2-2.5 g/kg/day; 4-10 years of age, >1.5-2 g/kg/day) and with Western Europe (n = 25 centres) giving the least (infants <1 year, >2-2.5 g/kg/day, 1-3 years of age, 1.5-2 g/kg/day; 4-10 years of age, 1-1.5 g/kg/day). Total protein prescription was similar in patients aged >10 years (1-1.5 g/kg/day) and maternal patients (1-1.5 g/kg/day). Conclusions: The amounts of total protein prescribed varied between European countries and appeared to be influenced by geographical region. In PKU, all gave higher than the recommended 2007 WHO/FAO/UNU safe levels of protein intake for the general population.

Subject headings and genre

MEDICIN OCH HÄLSOVETENSKAP Hälsovetenskap Annan hälsovetenskap hsv//swe
MEDICAL AND HEALTH SCIENCES Health Sciences Other Health Sciences hsv//eng
Phenylketonuria
Protein substitute
L-Amino acid supplements
Glycomacropeptide

Added entries (persons, corporate bodies, meetings, titles ...)

Ahring, K. (author)
Almeida, M. F. (author)
Assoun, M. (author)
Belanger Quintana, A. (author)
Bigot, S. (author)
Bihet, G. (author)
Malmberg, Karin BlomUppsala universitet,Institutionen för kostvetenskap(Swepub:uu)karbl392 (author)
Burlina, A. (author)
Bushueva, T. (author)
Caris, A. (author)
Chan, H. (author)
Clark, A. (author)
Clark, S. (author)
Cochrane, B. (author)
Corthouts, K. (author)
Dalmau, J. (author)
Dassy, M. (author)
De Meyer, A. (author)
Didycz, B. (author)
Diels, M. (author)
Dokupil, K. (author)
Dubois, S. (author)
Eftring, K. (author)
Ekengren, J. (author)
Ellerton, C. (author)
Evans, S. (author)
Faria, A. (author)
Fischer, A. (author)
Ford, S. (author)
Freisinger, P. (author)
Gizewska, M. (author)
Gokmen-Ozel, H. (author)
Gribben, J. (author)
Gunden, F. (author)
Heddrich-Ellerbrok, M. (author)
Heiber, S. (author)
Heidenborg, C. (author)
Jankowski, C. (author)
Janssen-Regelink, R. (author)
Jones, I. (author)
Jonkers, C. (author)
Joerg-Streller, M. (author)
Kaalund-Hansen, K. (author)
Kiss, E. (author)
Lammardo, A. M. (author)
Lang, K. (author)
Lier, D. (author)
Lilje, R. (author)
Lowry, S. (author)
Luyten, K. (author)
MacDonald, A. (author)
Meyer, U. (author)
Moor, D. (author)
Pal, A. (author)
Robert, M. (author)
Robertson, L. (author)
Rocha, J. C. (author)
Rohde, C. (author)
Ross, K. (author)
Saruhan, S. (author)
Sjoqvist, E. (author)
Skeath, R. (author)
Stoelen, L. (author)
Ter Horst, N. M. (author)
Terry, A. (author)
Timmer, C. (author)
Tuncer, N. (author)
Vande Kerckhove, K. (author)
van der Ploeg, L. (author)
van Rijn, M. (author)
van Spronsen, F. J. (author)
van Teeffelen-Heithoff, A. (author)
van Wegberg, A. (author)
van Wyk, K. (author)
Vasconcelos, C. (author)
Vitoria, I. (author)
Wildgoose, J. (author)
Webster, D. (author)
White, F. J. (author)
Zweers, H. (author)
Uppsala universitetInstitutionen för kostvetenskap (creator_code:org_t)

Related titles

In:Molecular Genetics and Metabolism: Elsevier BV115:1, s. 17-221096-71921096-7206

Internet link

Find in a library

Molecular Genetics and Metabolism (Search for host publication in LIBRIS)

To the university's database

Find more in SwePub

By the author/editor: Aguiar, A.; Ahring, K.; Almeida, M. F.; Assoun, M.; Belanger Quintan ...; Bigot, S.; show more...; Bihet, G.; Malmberg, Karin ...; Burlina, A.; Bushueva, T.; Caris, A.; Chan, H.; Clark, A.; Clark, S.; Cochrane, B.; Corthouts, K.; Dalmau, J.; Dassy, M.; De Meyer, A.; Didycz, B.; Diels, M.; Dokupil, K.; Dubois, S.; Eftring, K.; Ekengren, J.; Ellerton, C.; Evans, S.; Faria, A.; Fischer, A.; Ford, S.; Freisinger, P.; Gizewska, M.; Gokmen-Ozel, H.; Gribben, J.; Gunden, F.; Heddrich-Ellerbr ...; Heiber, S.; Heidenborg, C.; Jankowski, C.; Janssen-Regelink ...; Jones, I.; Jonkers, C.; Joerg-Streller, ...; Kaalund-Hansen, ...; Kiss, E.; Lammardo, A. M.; Lang, K.; Lier, D.; Lilje, R.; Lowry, S.; Luyten, K.; MacDonald, A.; Meyer, U.; Moor, D.; Pal, A.; Robert, M.; Robertson, L.; Rocha, J. C.; Rohde, C.; Ross, K.; Saruhan, S.; Sjoqvist, E.; Skeath, R.; Stoelen, L.; Ter Horst, N. M.; Terry, A.; Timmer, C.; Tuncer, N.; Vande Kerckhove, ...; van der Ploeg, L ...; van Rijn, M.; van Spronsen, F. ...; van Teeffelen-He ...; van Wegberg, A.; van Wyk, K.; Vasconcelos, C.; Vitoria, I.; Wildgoose, J.; Webster, D.; White, F. J.; Zweers, H.; show less...

About the subject

MEDICAL AND HEALTH SCIENCES: MEDICAL AND HEAL ...; and Health Sciences; and Other Health Sci ...

Articles in the publication: Molecular Geneti ...

By the university: Uppsala University

Search outside SwePub

Extend your search to:: Google; Google Book Search; Google Scholar

Kungliga biblioteket hanterar dina personuppgifter i enlighet med EU:s dataskyddsförordning (2018), GDPR. Läs mer om hur det funkar här.
Så här hanterar KB dina uppgifter vid användning av denna tjänst.

LIBRIS.kb.se