Sökning: id:"swepub:oai:DiVA.org:oru-6968" > Budd-Chiari syndrom...
Fältnamn | Indikatorer | Metadata |
---|---|---|
000 | 05765naa a2200685 4500 | |
001 | oai:DiVA.org:oru-6968 | |
003 | SwePub | |
008 | 090527s2009 | |||||||||||000 ||eng| | |
009 | oai:lup.lub.lu.se:951b0ac1-459a-44c5-b21c-ff1f46f90063 | |
009 | oai:DiVA.org:uu-153473 | |
009 | oai:DiVA.org:liu-16408 | |
024 | 7 | a https://urn.kb.se/resolve?urn=urn:nbn:se:oru:diva-69682 URI |
024 | 7 | a https://doi.org/10.1111/j.1478-3231.2008.01838.x2 DOI |
024 | 7 | a https://lup.lub.lu.se/record/13133112 URI |
024 | 7 | a https://urn.kb.se/resolve?urn=urn:nbn:se:uu:diva-1534732 URI |
024 | 7 | a https://urn.kb.se/resolve?urn=urn:nbn:se:liu:diva-164082 URI |
040 | a (SwePub)orud (SwePub)lud (SwePub)uud (SwePub)liu | |
041 | a engb eng | |
042 | 9 SwePub | |
072 | 7 | a ref2 swepub-contenttype |
072 | 7 | a art2 swepub-publicationtype |
100 | 1 | a Rajani, Rupeshu Linköpings universitet,Gastroenterologi och hepatologi,Hälsouniversitetet4 aut0 (Swepub:liu)rupra58 |
245 | 1 0 | a Budd-Chiari syndrome in Sweden :b epidemiology, clinical characteristics and survival - an 18-year experience |
264 | 1 | a Oxford :b Blackwell Munksgaard,c 2009 |
338 | a print2 rdacarrier | |
520 | a BACKGROUND: The exact incidence and prevalence of Budd-Chiari syndrome (BCS) is unknown in the general population. Published reports differ in terms of the clinical characteristics, effects of therapy and survival. AIMS: To investigate the epidemiology, clinical presentation and survival in patients with BCS. METHODS: Retrospective multicentre study in Sweden reviewing the medical records of all patients with BCS 1986-2003, identified from the computerised diagnosis database of 11 hospitals, including all university hospitals and liver transplantation centres. RESULTS: Forty-three patients with BCS were identified, of whom nine (21%) had concomitant portal vein thrombosis. The mean age-standardised incidence and prevalence rates in 1990-2001 were calculated to be 0.8 per million per year and 1.4 per million inhabitants respectively. Myeloproliferative disorders (38%), thrombophilic factors (31%) and oral contraceptives (30%) were common aetiological factors. Two or more risk factors were present in 44%. In 23%, no risk factor was evident. The median follow-up time was 2.7 years. Seventy-two percent were on anticoagulant therapy during follow-up. Transjugular intrahepatic portosystemic shunting, surgical shunting procedures and liver transplantation were performed in 4, 6 and 18 patients respectively. Nineteen patients died. The overall transplantation-free survival at 1, 5 and 10 years was 47, 28 and 17% respectively. CONCLUSIONS: Budd-Chiari syndrome is a rare disorder; the mean age-standardised incidence and prevalence rates in Sweden in 1990-2001 were calculated to be 0.8 per million per year and 1.4 per million inhabitants respectively. The presence of a myeloproliferative disorder was a common aetiological factor in our cohort and about half of the patients had a multifactorial aetiology. The transplantation-free survival was poor. | |
650 | 7 | a MEDICIN OCH HÄLSOVETENSKAPx Klinisk medicinx Gastroenterologi0 (SwePub)302132 hsv//swe |
650 | 7 | a MEDICAL AND HEALTH SCIENCESx Clinical Medicinex Gastroenterology and Hepatology0 (SwePub)302132 hsv//eng |
650 | 7 | a MEDICIN OCH HÄLSOVETENSKAPx Klinisk medicinx Reumatologi och inflammation0 (SwePub)302102 hsv//swe |
650 | 7 | a MEDICAL AND HEALTH SCIENCESx Clinical Medicinex Rheumatology and Autoimmunity0 (SwePub)302102 hsv//eng |
653 | a MEDICINE | |
653 | a MEDICIN | |
653 | a Gastroenterology | |
653 | a Gastroenterologi | |
653 | a Medicine | |
653 | a Medicin | |
653 | a hepatic vein thrombosis | |
653 | a Budd-Chiari syndrome | |
653 | a epidemiology | |
653 | a risk factors | |
653 | a prognosis | |
700 | 1 | a Melin, Toru University Hospital, Lund4 aut |
700 | 1 | a Björnsson, Einaru Sahlgrenska University Hospital, Göteborg4 aut |
700 | 1 | a Broomé, Ulrikau Karolinska University Hospital, Stockholm4 aut |
700 | 1 | a Sangfelt, Peru University Uppsala Hospital, Uppsala4 aut |
700 | 1 | a Danielsson, Åkeu Umea University Hospital, Umeå4 aut |
700 | 1 | a Gustavsson, Andersu Örebro universitet,Hälsoakademin,University Hospital, Örebro4 aut0 (Swepub:oru)argn |
700 | 1 | a Grip, Olofu Lund University,Lunds universitet,Enheten för kroniska inflammatoriska och degenerativa sjukdomar,Forskargrupper vid Lunds universitet,Chronic Inflammatory and Degenerative Diseases Research Unit,Lund University Research Groups,Malmö University Hospital, Malmö4 aut0 (Swepub:lu)medf-ogr |
700 | 1 | a Svensson, Hansu Vrinnevi Hospital, Norrköping4 aut |
700 | 1 | a Lööf, Larsu Uppsala universitet,Centrum för klinisk forskning, Västerås,Västerås City Hospital, Västerås4 aut0 (Swepub:uu)larsloof |
700 | 1 | a Wallerstedt, Svenu Östra Hospital, Gothenberg4 aut |
700 | 1 | a Almer, Svenu Östergötlands Läns Landsting,Linköpings universitet,Gastroenterologi och hepatologi,Hälsouniversitetet,Endokrin- och magtarmmedicinska kliniken US4 aut0 (Swepub:liu)sveal38 |
710 | 2 | a Linköpings universitetb Gastroenterologi och hepatologi4 org |
773 | 0 | t Liver international (Print)d Oxford : Blackwell Munksgaardg 29:2, s. 253-259q 29:2<253-259x 1478-3223x 1478-3231 |
856 | 4 | u http://dx.doi.org/10.1111/j.1478-3231.2008.01838.xy FULLTEXT |
856 | 4 8 | u https://urn.kb.se/resolve?urn=urn:nbn:se:oru:diva-6968 |
856 | 4 8 | u https://doi.org/10.1111/j.1478-3231.2008.01838.x |
856 | 4 8 | u https://lup.lub.lu.se/record/1313311 |
856 | 4 8 | u https://urn.kb.se/resolve?urn=urn:nbn:se:uu:diva-153473 |
856 | 4 8 | u https://urn.kb.se/resolve?urn=urn:nbn:se:liu:diva-16408 |
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