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LIBRIS Formathandbok  (Information om MARC21)
FältnamnIndikatorerMetadata
00003928naa a2200613 4500
001oai:DiVA.org:uu-235521
003SwePub
008141105s2014 | |||||||||||000 ||eng|
009oai:prod.swepub.kib.ki.se:129790070
024a https://urn.kb.se/resolve?urn=urn:nbn:se:uu:diva-2355212 URI
024a https://doi.org/10.1182/blood-2013-09-5279032 DOI
024a http://kipublications.ki.se/Default.aspx?queryparsed=id:1297900702 URI
040 a (SwePub)uud (SwePub)ki
041 a engb eng
042 9 SwePub
072 7a ref2 swepub-contenttype
072 7a art2 swepub-publicationtype
100a Geyer, Holly L.4 aut
2451 0a Distinct clustering of symptomatic burden among myeloproliferative neoplasm patients :b retrospective assessment in 1470 patients
264 1b American Society of Hematology,c 2014
338 a print2 rdacarrier
520 a Symptom burden in myeloproliferative neoplasms (MPNs) is heterogeneous even among patients within the same MPN diagnosis. Using cluster analysis from prospectively gathered symptom burden data in 1470 international patients with essential thrombocythemia (ET), polycythemia vera (PV), or myelofibrosis (MF), we assessed for the presence of clusters and relationship to disease features and prognosis. In MF (4 clusters identified), clusters significantly differed by Dynamic International Prognostic Scoring System (DIPSS) risk (P < .001), leukopenia (P = .009), thrombocytopenia (P < .001), and spleen size (P = .02). Although an association existed between clusters and DIPSS risk, high symptom burden was noted in some low and intermediate-1-risk MF patients. In PV (5 clusters identified), total symptom score increased across clusters (P < .001), but clusters did not significantly differ by PV risk or the risk assessment variable of age. Among ET patients (5 clusters identified), clusters differed by gender (P = .04), anemia (P = .01), and prior hemorrhage (P = .047). Total symptom score increased across clusters (P < .001), but clusters did not significantly differ by International Prognostic Score for ET risk including the risk assessment variables. Significant symptom heterogeneity exists within each MPN subtype, sometimes independent of disease features or prognosis.
650 7a MEDICIN OCH HÄLSOVETENSKAPx Klinisk medicinx Hematologi0 (SwePub)302022 hsv//swe
650 7a MEDICAL AND HEALTH SCIENCESx Clinical Medicinex Hematology0 (SwePub)302022 hsv//eng
700a Scherber, Robyn M.4 aut
700a Dueck, Amylou C.4 aut
700a Kiladjian, Jean-Jacques4 aut
700a Xiao, Zhijian4 aut
700a Slot, Stefanie4 aut
700a Zweegman, Sonja4 aut
700a Sackmann, Federico4 aut
700a Kerguelen Fuentes, Ana4 aut
700a Hernandez-Maraver, Dolores4 aut
700a Doehner, Konstanze4 aut
700a Harrison, Claire N.4 aut
700a Radia, Deepti4 aut
700a Muxi, Pablo4 aut
700a Besses, Carlos4 aut
700a Cervantes, Francisco4 aut
700a Johansson, Peter L.4 aut
700a Andreasson, Bjorn4 aut
700a Rambaldi, Alessandro4 aut
700a Barbui, Tiziano4 aut
700a Vannucchi, Alessandro M.4 aut
700a Passamonti, Francesco4 aut
700a Samuelsson, Janu Karolinska Institutet4 aut
700a Birgegård, Gunnaru Uppsala universitet,Hematologi4 aut0 (Swepub:uu)gunnarbg
700a Mesa, Ruben A.4 aut
710a Karolinska Institutetb Hematologi4 org
773t Bloodd : American Society of Hematologyg 123:24, s. 3803-3810q 123:24<3803-3810x 0006-4971x 1528-0020
856u https://europepmc.org/articles/pmc4067502
8564 8u https://urn.kb.se/resolve?urn=urn:nbn:se:uu:diva-235521
8564 8u https://doi.org/10.1182/blood-2013-09-527903
8564 8u http://kipublications.ki.se/Default.aspx?queryparsed=id:129790070

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