Search: WFRF:(Smith Alison)
> (2005-2009) >
Guidelines for Mana...
Guidelines for Management of Scoliosis in Rett Syndrome Patients Based on Expert Consensus and Clinical Evidence
-
- Downs, Jenny (author)
- University of Western Australia
-
- Bergman, Anke (author)
- University of Western Australia
-
- Carter, Philippa (author)
- University of Western Australia
-
show more...
-
- Anderson, Alison (author)
- University of Western Australia
-
- M Palmer, Greta (author)
- Royal Childrens Hospital, Melbourne
-
- Roye, David (author)
- Columbia University
-
- van Bosse, Harold (author)
- Shriners Hospital Children
-
- Bebbington, Ami (author)
- University of Western Australia
-
- Larsson, Eva-Lena (author)
- Linköpings universitet,Hälsa, Aktivitet, Vård (HAV),Hälsouniversitetet
-
- Smith, Brian G (author)
- Yale University
-
- Baikie, Gordon (author)
- Royal Childrens Hospital, Melbourne
-
- Fyfe, Sue (author)
- Curtin University of Technology
-
- Leonard, Helen (author)
- University of Western Australia
-
show less...
-
(creator_code:org_t)
- 2009
- 2009
- English.
-
In: SPINE. - 0362-2436. ; 34:17, s. E607-E617
- Related links:
-
https://liu.diva-por... (primary) (Raw object)
-
show more...
-
https://urn.kb.se/re...
-
https://doi.org/10.1...
-
show less...
Abstract
Subject headings
Close
- Study Design. Modified Delphi technique. Objective. To develop guidelines for the clinical management of scoliosis in Rett syndrome through evidence review and consensus expert panel opinion. Summary of Background Data. Rett syndrome is a rare disorder and clinical expertise is thus with small case series. Scoliosis is a frequent association and the evidence base dealing with scoliosis management in this syndrome is limited. Parents of affected girls and women have expressed needs for more information about scoliosis and Rett syndrome. Methods. An initial draft of scoliosis guidelines was created based on literature review and open-ended questions where the literature was lacking. Perspectives of four parents of Rett syndrome patients informed this initial draft. Access to an online and a Microsoft Word formatted version of the draft were then sent to an international, multidisciplinary panel of clinicians via e-mail with input sought using a 2-stage modified Delphi process to reach consensus agreement. Items included clinical monitoring and intervention before the diagnosis of scoliosis; monitoring after the diagnosis of scoliosis; imaging; therapy and conservative management; bracing; and preoperative, surgical, and postoperative considerations. Results. The first draft contained 71 statements, 65 questions. The second draft comprised 88 items with agreement to strong agreement achieved on 85, to form the final guideline document. A comprehensive, life-span approach to the management of scoliosis in Rett syndrome is recommended that takes into account factors such as physical activity, posture, nutritional and bone health needs. Surgery should be considered when the Cobb angle is approximately 40 to 50 and must be supported by specialist management of anesthesia, pain control, seizures, and early mobilization. Conclusion. Evidence-and consensus-based guidelines were successfully created and have the potential to improve care of a complex comorbidity in a rare condition and stimulate research to improve the current limited evidence base.
Keyword
- Rett syndrome
- scoliosis
- neuromuscular diseases
- Delphi technique
- practice guideline
- MEDICINE
- MEDICIN
Publication and Content Type
- ref (subject category)
- art (subject category)
Find in a library
-
SPINE
(Search for host publication in LIBRIS)
To the university's database
- By the author/editor
-
Downs, Jenny
-
Bergman, Anke
-
Carter, Philippa
-
Anderson, Alison
-
M Palmer, Greta
-
Roye, David
-
show more...
-
van Bosse, Harol ...
-
Bebbington, Ami
-
Larsson, Eva-Len ...
-
Smith, Brian G
-
Baikie, Gordon
-
Fyfe, Sue
-
Leonard, Helen
-
show less...
- Articles in the publication
-
SPINE
- By the university
-
Linköping University