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Heart transplantati...
Heart transplantation in arrhythmogenic right ventricular cardiomyopathy - Experience from the Nordic ARVC Registry
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- Gilljam, Thomas (författare)
- Gothenburg University,Göteborgs universitet,Institutionen för medicin,Institute of Medicine
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- Haugaa, Kristina H. (författare)
- Oslo University Hospital, Norway; University of Oslo, Norway
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- Jensen, Henrik K. (författare)
- Aarhus University Hospital,Aarhus University, Denmark; Aarhus University, Denmark
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- Svensson, Anneli (författare)
- Linköpings universitet,Linköping University,Avdelningen för kardiovaskulär medicin,Medicinska fakulteten,Region Östergötland, Kardiologiska kliniken US
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- Bundgaard, Henning (författare)
- Copenhagen University Hospital,University of Copenhagen, Denmark
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- Hansen, Jim (författare)
- University of Copenhagen, Denmark
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- Dellgren, Göran, 1961 (författare)
- Gothenburg University,Göteborgs universitet,Institutionen för medicin, avdelningen för molekylär och klinisk medicin,Institute of Medicine, Department of Molecular and Clinical Medicine
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- Gustafsson, Finn (författare)
- University of Copenhagen, Denmark
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- Eiskjær, Hans (författare)
- Aarhus University Hospital,Aarhus University, Denmark; Aarhus University, Denmark
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- Andreassen, Arne K. (författare)
- Norwegian Radium Hospital,Oslo University Hospital, Norway
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- Sjögren, Johan (författare)
- Lund University,Lunds universitet,Thoraxkirurgi,Sektion II,Institutionen för kliniska vetenskaper, Lund,Medicinska fakulteten,Thoracic Surgery,Section II,Department of Clinical Sciences, Lund,Faculty of Medicine,Skåne University Hospital,Lund University, Sweden
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- Edvardsen, Thor (författare)
- Oslo University Hospital, Norway; University of Oslo, Norway
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- Holst, Anders G. (författare)
- University of Copenhagen, Denmark
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- Svendsen, Jesper Hastrup (författare)
- University of Copenhagen, Denmark
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- Platonov, Pyotr G. (författare)
- Lund University,Lunds universitet,Kardiologi,Sektion II,Institutionen för kliniska vetenskaper, Lund,Medicinska fakulteten,Cardiology,Section II,Department of Clinical Sciences, Lund,Faculty of Medicine,Lund University, Sweden; Skåne University Hospital, Sweden
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(creator_code:org_t)
- Elsevier BV, 2018
- 2018
- Engelska.
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Ingår i: International Journal of Cardiology. - : Elsevier BV. - 0167-5273 .- 1874-1754. ; 250, s. 201-206
- Relaterad länk:
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http://dx.doi.org/10...
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https://www.duo.uio....
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https://lup.lub.lu.s...
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https://doi.org/10.1...
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https://urn.kb.se/re...
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https://gup.ub.gu.se...
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Abstract
Ämnesord
Stäng
- Objective: There is a paucity of data on heart transplantation (HTx) in patients with arrhythmogenic right ventricular cardiomyopathy (ARVC), and specific recommendations on indications for listing ARVC patients for HTx are lacking. In order to delineate features pertinent to HTx assessment, we explored the pre-HTx characteristics and clinical history in a cohort of ARVC patients who received heart transplants. Methods: Data from 31 ARVC/HTx patients enrolled in the Nordic ARVC Registry, transplanted between 1988 and 2014 at a median age of 46. years (14-65), were compared with data from 152 non-transplanted probands with Definite ARVC according to 2010 Task Force Criteria from the same registry. Results: The HTx patients were younger at presentation, median 31 vs. 38. years (p = 0.001). There was no difference in arrhythmia-related events. The indication for HTx was heart failure in 28 patients (90%) and ventricular arrhythmias in 3 patients (10%). During median follow-up of 4.9. years (0.04-28), there was one early death and two late deaths. Survival was 91% at 5. years after HTx. Age at first symptoms under 35. years independently predicted HTx in our cohort (OR = 7.59, 95% CI 2.69-21.39, p <. 0.001). Conclusion: HTx in patients with ARVC is performed predominantly due to heart failure. This suggests that current 2016 International Society for Heart and Lung Transplantation heart transplant listing recommendations for other cardiomyopathies could be applicable in many cases when taking into account the haemodynamic consequences of right ventricular failure in conjunction with ventricular arrhythmia.
Ämnesord
- MEDICIN OCH HÄLSOVETENSKAP -- Klinisk medicin -- Kardiologi (hsv//swe)
- MEDICAL AND HEALTH SCIENCES -- Clinical Medicine -- Cardiac and Cardiovascular Systems (hsv//eng)
Nyckelord
- Arrhythmogenic right ventricular cardiomyopathy
- Heart transplantation
- Arrhythmogenic right ventricular cardiomyopathy; Heart transplantation
Publikations- och innehållstyp
- art (ämneskategori)
- ref (ämneskategori)
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Gilljam, Thomas
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Haugaa, Kristina ...
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Jensen, Henrik K ...
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Svensson, Anneli
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Bundgaard, Henni ...
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Hansen, Jim
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Dellgren, Göran, ...
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Gustafsson, Finn
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Eiskjær, Hans
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Andreassen, Arne ...
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Sjögren, Johan
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Edvardsen, Thor
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Holst, Anders G.
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Svendsen, Jesper ...
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Platonov, Pyotr ...
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