ADHD symptoms and insistence on sameness in Prader-Willi syndrome

• Background: Apart from a pervasive eating disorder, the Prader-Willi (PWS) syndrome is characterised by a distinct behavioural profile comprising maladap-tive behaviours, obsessive-compulsive traits and skin picking, all included in the PWS behavioural phenotype. This study presents a further delineation of this characteristic behavioural profile by screening for indices of executive dysfunc-tions related to attention-deficit/hyperactivity disorder (ADHD), immature com-pulsive-like adherence to sameness and skin picking and how these features ag-gregate into symptom constellations in children and adolescents with PWS. Method: Parents of 58 individuals with PWS (aged 5 to 18 years) participated by completing Childhood Routines Inventory (CRI) and Conners Parent Rating Scale (CPRS-48). Results: Results showed that indices of ADHD and excessive in-sistence on sameness were common, comorbid and of early onset. They were both associated with conduct problems. Skin picking, appearing as a single and co-morbid symptom, was less associated with child-like compulsions and ADHD-related problems Conclusions: Findings are discussed in terms of further re-search in executive dysfunctions in PWS.

Ämnesord

SAMHÄLLSVETENSKAP  -- Psykologi (hsv//swe)

SOCIAL SCIENCES  -- Psychology (hsv//eng)

Nyckelord

ADHD

CPRS-48

executive functions

Prader-Willi syndrome

Publikations- och innehållstyp

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